Coexistence of the Renal Fibromuscular Dysplasia and Familial Adenomatous Polyposis |
Jeong Min Cha, M.D.1, Kang Won Lee, M.D.1, Jae Hoon Lee, M.D.1, Yu Min Lee, M.D.1 Sung Won Jung, M.D.1, Ji Eun Lee, M.D.1, Jin Ho Shin, M.D.1 , Ju Hung Song, M.D.1 Hun Su Kim, M.D.2 , Hyang Jung Cho, M.D.2 and Seon Ho Ahn, M.D.1 |
Department of Internal Medicine1 and Pathology2 Wonkwang University School of Medicine, Iksan, Korea |
증례 : 가족성 선종성 용종증 환자에서 병발된 신동맥의 섬유근성 이형성증 1예 |
차정민1 이강원1 이재훈1 이유민1 정성원1 이지은1 신진호1 송주흥1 김헌수2 조향정2 안선호1 |
원광대학교 의과대학 내과학 교실, 병리학 교실1 |
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Abstract |
Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disease that most commonly affects the renal and internal carotid arteries. A Familial adenomatous polyposis (FAP) is characterized by hundreds of adenomatous colorectal polyps, with an almost inevitable progression to colorectal cancer.
A 19-year-old woman with history of total colectomy as a result of familial adenomatous polyposis presented with high blood pressure incidentally. Abdominal CT scan showed "string of beads" appearance of right renal artery. Percutaneous transluminal renal angioplasty was performed and then hypertension was improved.
To our knowledge, there has been no previous case report of secondary renovascular hypertension resulting from fibromuscular dysplasia in patients with FAP. Here, we report a patient with a review of the literature.
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Key Words:
Fibromuscular dysplasia (FMD), Familial adenomatous polyposis (FAP), Renovascular hypertension |
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